Zahid Gul, Fahad Liaqat, Huma Ambreen Khan, Syed Zia Ul Haq, Momina Tehreem


Congenital lobar emphysema (CLE) is a rare form of congenital malformation of the lungs that is characterized by over distension of a lobe of lung due to partial obstruction of the bronchus. The case that we are reporting is a 7 months old male patient admitted in the pediatric department with sign and symptoms of bronchiolitis/ bronchopneumonia.
The patient was investigated which shows, CXR showed partial consolidation of right upper and lower lobe and lobar emphysema (left upper lobe). As additional diagnostic method, thorax computerized tomography was also done. The affected lobe was the left upper lobe. The baby was treated conservatively and discharged home safely followed by regular follow up visits.


Congenital emphysema; Emphysema

Full Text:



Canals RJ, Boix OJ, Peiro JL, Ezzeding M, Cobis BN, Linan CS, et al. Congenital lobar emphysema: Report of 38 cases. Circ Peditr 1994; 7:97-101.

Fatureto MC, Ferreira DP, Ferraz DA. Congenital lobar emphysema: study of a case. Rev Port Pneumol 2008; 14:893-6.

Stigers K B, Woodring JH, Kanga JF. The clinical and imaging spectrum of findings in patients with congenital lobar emphysema. Pediatr Pulmonlo 1991; 14:160-70.

Konan Blé R, Coste K, Blanc P. Congenital lobar emphysema: a rare etiology of hyperechoic lung. Gynecol Obstet Fertil 2008; 36:529-31.

Chao MC, Karamzadeh AM, Ahuja G: Congenital lobar emphy-sema. Int J Pediatr Otorhinolaryngol 2005; 9:549-54.

Khemiri M, Ouederni M, Ben Mansour F, Barasaoui S. Bronchogenic cyst: an uncommon cause of congenital lobar emphysema. Respir Med 2008; 102:1663-6.

Dogan R, Dogan OF, Yilmaz M, Passaglu I, Kliper N, Ozecelik U, et al. Surgical management of Infant with congenital lobar emphysema and concomitant heart disease. Heart Surg Forum 2004; 7:644-9.

Mei-Zahav M, Konen O, Manson D, Langer JC. Is congenital lobar emphysema a surgical disease? J Pediatr Surg 2006; 41:1058-61.

Behrman R, Kliegman R. Nelson Textbook of Pediatrics. Vol 2, 19th ed. Philadelphia: W.B. Saunders Elsevier; 2010. p. 1742-1803.

Paramesh H. Textbook of Practical Pediatric Pulmonology. 4th ed. Philadelphia: Mc Grow Hill; 2009. p. 70-9.

Lierl M. Congenital abnormalities. In: Hilman B.C, editor. Pediatric Respiratory Disease: Diagnosis and Treatment. 1st ed. Philadelphia: W.B. Saunders; 1993. p. 468-72.

Krummel TM. Congenital malformation of the lower respiratory tract in: Chernick V, Boat TF, editors. Kendig’s Disorders of the Respiratory Tract in Children. 6th ed. Philadelphia: W.B. Saunders; 1998; p. 310-1.

Lincoln JC, Stark J, Subramanian S, Aberdeen E, Bonham-Carter RE, Berry CL, et al. Congenital lobar emphysema. Ann Surg 1971; 173:55-62.

Carrol ED, Campbell ME, Shaw BN, Pilling DW. Congenital lobar emphysema in congenital cytomegalovirus infection. Pediatr Radiol1996; 26: 900-2.

Martin R, Fanaroff A, Walsh M. Fanaroff and Martin's Neonatal-Perinatal Medicine. 9th ed. 2008: 1002- 3.

Dewan RK, Kesieme EB, Sisodia A, Ramchandani R, Kesieme CN. Congenital malformation of lung parenchyma: 15 years’ experience in a thoracic surgical unit. Indian J Chest Dis Allied Sci 2012; 54:105-9.

Toyoshima M, Suda T, Chida K. Asymptomatic congenital lobar emphysema in a young adult. Intern Med 2012; 51:2839-40.

Lincoln JC, Stark J, Subramanian S, Aberdeen E, Bonham-Carter RE, Berry CL, et al. Congenital lobar emphysema. Ann Surg1971; 173: 55-62.

Man DW, Hamdy MH, Hendry GM, Bisset WH, Forfar JO. Congenital lobar emphysema: problems in diagnosis and management. Arch Dis Child 1983; 58:709-12.

Ben Abdallah R, Bouthour H, Hellal Y, Ben Malek MR, Gharbi Y, Kaabar N. Congenital pulmonary malformations: clinical, radiological and treatment features. Tunis Med 2013;91:66-9.

Nath MP, Gupta S, Kumar A, Chakrabarty A. Congenital lobar emphysema in neonates: Anaesthetic challenges. Indian J Anaesth 2011; 55:280-3.

Shanti CM, Klein MD. Cystic lung disease Semin Pediatr Surg 2008; 17:2-8.

Chia CC, Huang SC, Liu MC, Se TY. Fetal congenital lobar emphysema. Taiwan J Obstet Gynecol 2007; 46:73-6.

Ang L, He XL, Zhang ZX. Congenital lobar emphysema complicated with right upper lung bronchial dysplasia in a case. Zhonghua Er Ke Za Zhi 2006; 44:956.


  • There are currently no refbacks.

Copyright (c) 2020 Zahid Gul, Fahad Liaqat, Huma Ambreen Khan, Syed Zia Ul Haq, Momina Tehreem

Creative Commons License
This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.